The expected approval of ICD-10 codes for familial hypercholesterolemia (FH) marks  a historic effort to prevent premature heart attacks and death  
The FH Foundation team at the ICD-10 Coordination Committee Meeting in 2014
 "Hopefully this will send a clear message to the medical community that
familial hypercholesterolemia is different.  
Those of us with FH need to be treated as the high risk population that we are."
  - Katherine Wilemon
  Founder and CEO
   The FH Foundation
In response to the FH Foundation's 2014 application, the International Classification of Diseases 10 (ICD) codes for Familial Hypercholesterolemia (FH) have been  included in the interim list of codes that are expected to be approved  June of 2016.

Although FH is one of the most common life-threatening genetic conditions affecting all races and ethnicities, there has been no specific diagnosis code to differentiate FH from other forms of hypercholesterolemia. Two codes are expected to be approved for Familial Hypercholesterolemia (E78.01) and Family History of FH (Z83.42). The FH ICD-10 codes are scheduled to become effective on October 1, 2016.

"We are delighted at the increased recognition a distinct ICD-10 code will bring to FH.  We believe that this will allow individuals 
with FH to get the care they need and deserve."

                     - Joshua Knowles, MD
                        Cardiologist at Stanford University
                               Chief Medical Advisor to the FH Foundation