response to the FH Foundation's 2014 application, the International Classification of Diseases 10 (ICD) codes for Familial Hypercholesterolemia (FH) have been
included in the interim list of codes that are expected to be approved
June of 2016.
Although FH is one of the most common life-threatening genetic conditions affecting all races and ethnicities, there has been no specific diagnosis code to differentiate FH from other forms of hypercholesterolemia. Two codes are expected to be approved for Familial Hypercholesterolemia (E78.01) and Family History of FH (Z83.42). The FH ICD-10 codes are scheduled to become effective on October 1, 2016.